Clinical and genetic analysis of two Chinese families with benign familial neonatal convulsions

Benignfamilialneonatalconvulsions(BFNC)is arareautosomaldominantinheritedepilepsysyn dromecharacterizedbyunprovokedpartialorgeneral izedseizures.Theseizuresusuallyoccurfromthesec onddayofbirthtothesixthmonthandremitsponta neouslyafterseveralweekstomonths.Mostindivid ualsareseizure freebytheageofsixmonths.The serumchemistryandneuroradiologicalexaminations,interictalelectroencephalogram(EEG),andpsy chomotordevelopmentareusuallynormal.However,10%to15%ofpatientshavetheriskofseizurere currencela…     

Olfaction in Lepidoptera

Odours play a very important role in the life of insects belonging to the order Lepidoptera. In the present paper, a review is given of the current knowledge of morphology, development and function of the olfactory system in larval and adult moths and butterflies. Research regarding both the antennal and accessory olfactory pathways, as well as both the pheromone and the host odour detecting systems, is reviewed.     

遥感技术在土地利用动态变化中的应用研究

动态变化监测已成为遥感应用的一个主要方面,多时相、多种类型的传感器对同一地区进行定期或不定期地资源与环境调查,能及时、准确、宏观地反映客观情况;为土地资源的规划和治理提供科学依据.     

基于降低时间分辨率转换编码模型的运动估值方法

分析了基于降低时间分辨率转换编码模型的运动估值问题,给出了双线性内插法、前向主向量选择法和前向向量法的理论分析结果和实验结果。实验结果表明:前向向量法比其它两种方法不仅提高了图像的信噪比,而且减少了计算量。     

高发性大发作癫痫病人SCE频率的研究

本文对一个癫痫高发家系中6名高发性大发作癫痫病人作了姊妹染色单体互换(SCE)频率的观察,并与10名正常人进行比较研究。经统计分析,病人的SCE频率明显高于正常人,表明癫痫的高发性大发作与其DNA的不稳定或损伤有关。     

Spatial and temporal variations of zooplankton composition and quantity distribution in the upper waters around Nansha Islands

This study aims to examine spatial and temporal variations of zooplankton species composition, density and biomass distribution and community structure, based on the data obtained from three separate cruises carded out in November 1997, April and July 1999. Results show that 244 species of zooplankton and 8 groups of planktonic larvae were identified, which were dominated by copepods, followed by amphipods, ostracods and medusae. The total species were 201 and 198 for the cruises of November 1997 and July 1999, respectively, and no obvious seasonal variation of species richness was observed. The distribution of zooplankton species richness decreased from pelagic to coastal waters. Average richness of species in each station was higher in the cruises of November 1997（62） and April 1999（61） than in the cruise in July 1999 （56）, which was mainly a result from the pelagic or coastal water mass movement made by the monsoon. Zooplankton in the upper waters （0--100 m） around Nansha Islands belonged to the typical tropic pelagic fauna, most of them were pelagic warm-water species, followed by coastal warm-water species and euryhaline warm-water species. The number of dominant species ranged from 5 to 7 in each cruise. No obvious seasonal succession of dominant species was ob- served. Sagitta enflata, Cypridina narni, Cosmocalanus darwinii, Pleuromamma gracilis and Echino-pluteus larva were the main dominant species. The average of zooplankton biomass and density in three cruises were 31, 32, 28 mg·m^-3 and 31, 39, 35 ind·m^-3, respectively. Copepods were the most abundant, followed by chaetognaths. Zooplankton high biomass distributed mainly in the northwestern waters around Nansha Islands, and generally occurred in the areas of oceanic front and upweUing. The main reason for zooplankton quantity without obvious seasonal variation was the relative steady temperature dynamics in the waters around Nansha Islands.     

考虑丢包特性的无参考网络视频质量评估模型

针对相同丢包率条件下不同的包丢失集中度对视频质量影响不同的问题,提出一种考虑丢包特性并且不需要对视频解码的无参考网络视频质量评估模型.首先依据码流信息在压缩域计算视频的时域复杂度,然后在压缩域计算包丢失集中度和包丢失率对视频质量的影响因子.考虑到人眼视觉系统的空域掩盖效应和时域掩盖效应,进而提出由于丢包引起的视频质量下降的视频质量评估模型.该模型不需要对视频进行完全解码,具有资源开销小、实时性好的特点,适合对实时传输的视频流进行质量评估.实验结果表明,使用该视频质量评估模型测得的视频包丢失质量评分与其主观质量评分有很好的一致性,相比于国际标准G.1070中的丢包视频质量评价模型,无参考网络视频质量评价模型与主观质量评价的相关性平均提高了6.18%.     

基于DEA交叉模型的西部地区生态效率时空变化

建立基于DEA模型的生态效率投入产出指标体系,以2005-2009西部地区11个省份截面数据为样本,采用DEA交叉评价模型和空间对比分析方法,对西部地区生态效率进行时空差异研究.结果表明:从时间上看,西部地区生态效率总体上呈现出增加的趋势,省份之间的差异进一步扩大,其中,陕西一直处于首位,而宁夏一直处于末位.从空间上看,西部地区生态效率存在着明显的区域差异,东南区域整体上要高于西北区域,但是区域间的这种差异呈现出增大的趋势,生态效率分布的重心逐渐向区域中心集中,经济条件好的省份生态效率水平相对较高.最后,依据以上研究发现,提出了相应的建议.     

鄱阳湖不同形态氮的时空分布特征

通过调查鄱阳湖2010年水体中硝酸盐氮、氨氮及总氮浓度,分析不同形态氮的时空分布特征,并采用相关性分析法分析了2010年硝酸盐氮、氨氮及总氮三者的关系.结果表明:在时间分布上,2010年鄱阳湖水体总氮含量年平均值是1.50 mg/L,硝酸盐氮含量平均值为0.84 mg/L,氨氮含量年平均值是0.37 mg/L,丰水期不同形态氮的含量均明显低于枯水期;在空间分布上,枯水期硝酸盐氮、氨氮主航道中游含量较高,上、下游稍低.用相关性分析法分析知,2010年硝酸盐氮与总氮之间有显著的相关性,关联度分别达到0.99和0.95.减少硝酸盐氮与氨氮的输入有利于对富营养化的控制.     

近20年来黄河三角洲土地利用与覆被动态变化——以东营市为例

以黄河三角洲东营市为例,对东营市1989年、1999年、2009年三期遥感影像用ERDAS和ARCGIS软件进行融合、镶嵌、裁剪和解译,分析1989—2009的东营市土地利用／覆被变化．结果表明黄河三角洲东营市近二十年来建筑用地、水域、盐田、养殖水面、耕地面积呈总体增加趋势,而草地、未利用地、滩涂和林地呈现总体减少的趋势,其中盐田的增加速度最快,建设用地面积增加最大．1999—2009与1989—1999相比综合土地利用动态度和土地利用综合程度都提高了,土地利用更加集约化．