Erythrophagocytosis by cultured skin fibroblasts from patients with hereditary metabolic disorders |
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| Authors: | M Elleder E Hole?ková V Mandys |
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| Institution: | (1) 1st Department of Pathology, 1st Prague Medical Faculty, Charles University, Studni kova 2, 128 00 Prague 2;(2) Institute of Experimental Medicine, Czechoslovak Academy of Sciences, Prague, (Czechoslovakia) |
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| Abstract: | Phagocytosis of native allogenic red blood cells was observed in cultures of skin fibroblasts obtained from patients with neuronal ceroid-lipofuscinosis, Niemann-Pick disease type C and morbus Fabry. Occasional phagocytizing cells were observed in 9 other syndromes. Cells from three normal donors did not phagocytize. |
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| Keywords: | Erythrophagocytosis metabolic disorders cultured skin fibroblasts |
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