Further studies on hepatic acidic glycosaminoglycans in the Hurler syndrome |
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| Authors: | J A Kofoed A A Tocci A C Barceló |
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| Institution: | (1) Cátedra de Fisiología, Facultad de Odontología, Universidad de Buenos Aires, M.T. de Alvear 2142, Buenos Aires, Argentina;(2) Present address:  Carrena del Investigador Cientifico , Conicet, Argentina |
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| Abstract: | Summary Acid GAG were isolated from hepatic tissue from 3 patients with Hurler syndrome and 3 normal controls. Gross elevations in the uronic acid and hexosamine contents were found in Hurler livers compared with the normal ones. The total GAG concentration was significantly increased (about 25fold) in Hurler patients.This work was partially supported by research grants from the Conicet, Argentina. |
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